| ICD-10 Code | Description |
| D81.0 | Severe combined immunodeficiency [SCID] with reticular dysgenesis |
| D81.1 | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
| D81.2 | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
| D81.30 | Adenosine deaminase deficiency, unspecified |
| D81.31 | Severe combined immunodeficiency due to adenosine deaminase deficiency |
| D81.32 | Adenosine deaminase 2 deficiency |
| D81.39 | Other adenosine deaminase deficiency |
| D81.4 | Nezelof's syndrome |
| D81.5 | Purine nucleoside phosphorylase [PNP] deficiency |
| D81.6 | Major histocompatibility complex class I deficiency |
| D81.7 | Major histocompatibility complex class II deficiency |
| D81.810 | Biotinidase deficiency |
| D81.818 | Other biotin-dependent carboxylase deficiency |
| D81.819 | Biotin-dependent carboxylase deficiency, unspecified |
| D81.82 | Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
| D81.89 | Other combined immunodeficiencies |
| D81.9 | Combined immunodeficiency, unspecified |
